Immune Disorders Review Questions

Fill-In-The-Blank: these statements are conceptual; as such there may be other correct answers in addition to the ones provided.

     In humans, MHC molecules are called .

     MHC molecules come in thousands of different .

     Inappropriate immune reactions against foreign antigens are called , whereas reaction against self antigens are called .

     Rapid onset allergic reactions against things like cat saliva or ragweed are called type- or . These reactions are caused by the crosslinking of antibodies on the surface of .

     Degranulation of mast cells releases leukotrienes, prostaglandins and . On the skin, this degranulation cause , more formally known as .

     If these reactions go out of control, they can cause systemic .

     In contrast, slow onset allergies against things like poison oak or nickel are called type- or . These reactions are mediated by dendritic and .

     Rheumatic heart disease, where a self antigen is mistaken for a foreign antigen, is an example of .

     Tissue damage and/or infection can bring on autoimmune disease by uncovering hidden antigens AND providing that stimulate innate immunity.

     Soluble immune complexes are found in type- hypersensitivity reactions.

     Delayed-Type Hypersensitivity (DTH) reactions are also know as type- hypersensitivity reactions.

     Autoantibodies against bound (surface) antigens are found in type- hypersensitivity reactions.

     Immediate hypersensitivity due crosslinking of IgE on mast cells is found in type- hypersensitivity reactions.

     T-cells that inhibit autoimmune reactions are called T-cells.

     Severe Combined Immunodeficiency (SCID) is an example of a immunodeficiency.

     Steroids, TB, HIV, advanced cancer, and age can all cause immunodeficiency.

     Immunodeficient patients can develop infections.

     Transplanting a blood type A organ into a blood type B patient will result in rejection.

     Most transplant patients will undergo at least one bout of .

     Ultimately the only treatment for chronic rejection is .

Multiple Choice Questions:

     1) IgA deficiency is a fairly common and mild immunodeficiency. Many patients don't know they have it, but they may be at increase risk for:
Autoimmune Diseases
Mucosal Infections
Allergies
All of the above
     
Explanation: IgA has both immunoprotective and immunoinhibitory properties. Healthy mucosa is required for the prevention of allergic reactions. People with selective IgA deficiency may be at risk for any of these conditions.

     2) Recent studies of the Tsimane, an indigenous people of Bolivia, have shown that the incidence of allergies and asthma are non-existent, but the patients have markedly elevated levels of C-reactive protein (CRP), eosinophils, and serum IgE. The best explanation for these findings is:
Their hunter-gatherer existence ensures adequate exercise
They live far away from urban centers and have minimal exposure to pollutants
They are chronically infected with parasites (helminths)
They have a varied diet of fruits and vegetables but limited meat
     
Explanation: Although all 4 options are true statements, elevated CRP levels indicate an ongoing chronic inflammatory state. Increased eosinophils and IgE indicate exposure to parasites. There is some evidence to suggest that exposure to parasites minimizes the risk of developing allergies and autoimmune disease (the so-called "hygiene hypothesis")..

     3) Systemic mastocytosis is a disease where patients have far too many mast cells in their body. Which of the following are symptoms of the disease:
Urticaria (hives)
Diarrhea
Anaphylaxis
All of the above
     
Explanation: Degranulation of mast cells leads to type-I immediate hypersensitivity reactions. Systemically it can lead to anaphylaxis.

     4) You see a patient with autoimmune hemolytic anemia, an autoimmune disease characterized by autoantibodies that bind the surface of red blood cells (RBC) causing them to lyse. What type of hypersensitivity reaction is it:
type-I
type-II
type-III
type-IV
     
Explanation: Although RBCs are in the circulation they are not "soluble". Therefore this is a type-II reaction.

     5) You see a child who has been diagnosed with atopic dermatitis. You know that this skin condition is the result of:
IgE-mediated mast cell degranulation
IgA deficiency
Delayed-type hypersensitivity
A primary immunodeficiency
     
Explanation: Atopy or atopic refers to the propensity to have inappropriate type-I hypersensitivity reactions (due to IgE-mediated mast cell degranulation).

     6) Lupus patients often have immune complexes consisting of antibody and soluble, nuclear proteins in their blood. This is an example of what type of hypersensitivity?
Type I
Type II
Type III
Type IV
     
Explanation: Type III reactions involve soluble antigen and the formation of immune complexes

     7) SCID is short for...
Self Contained Immune Domain
Severe Combined Immune Deficiency
Sub Cutaneous Immune Deposit
Surface Complement Inhibition Disease
     
Explanation: SCID is a severe form of primary immunodeficiency

     8) Which of the following are NOT typically involved in Type IV hypersensitivity reactions?
Dendritic Cells
T-Cells
Mast Cells
B-Cells
Both C and D
     
Explanation: Type IV hypersensitivity reactions are due to the interactions of antigen, DCs, and T-cells.

     9) Two drugs that are helpful in treating acute type-I hypersensitivity reactions are:
Antihistamines (e.g. Benadryl)
Epinephrine (e.g. Epi-pen)
Anti IL-6 antibodies
Both A & B
     
Explanation: IgE-mediated degranulation of mast cells releases histamines which can be counteracted with anti-histamines. In severe systemic anaphylactic reactions, epinephrine is useful.

     10) Regulatory T cells are responsible for...
Bureaucratic red tape
Preventing autoimmune disease
Promoting type IV hypersensitivity reactions
Stimulating innate immune responses
     
Explanation: When stimulated by a specific peptide antigen, regulatory T-cells inhibit rather than promote immune reactions.

     11) Which of the following is true about acute cellular rejection?
It can occur within weeks / months after engraftment
It can be T-cell or antibody mediated
It can be controlled using immunosuppressive therapy
It can lead to chronic rejection
All of the above
     
Explanation: All are correct!

     12) Patients with group A strep infections (e.g. strep throat) are treated with antibiotics primarily to prevent...
Sepsis
Lupus
Rheumatic heart disease
Asthma
Goodpasture syndrome
     
Explanation: Group A strep contains a molecular mimic that cross-reacts with proteins found in the heart muscle & valves.

     13) A PPD reaction (T.B. test) is an example of which type of hypersensitivity reaction?
Type I
Type II
Type III
Type IV
     
Explanation: PPDs are a delayed type hypersensitivity reaction


Email a question, comment, or concern: robert.camp@yale.edu